ECHO 2013 / Hypertrophic Cardiomyopathy
.pdfEpidemiology of Hypertrophic
Cardiomyopathy–Related Death
Maron, Circulation. 2000;102:858-864.
Lakdawala, In
Garcia: Non-
Invasive
Cardiovascular
Imaging, LWW
2009
Genetic Testing in HCM
Boss, J Am Coll Cardiol 2009;54:201-11
HCM
Myocardial Fibrosis and risk of sudden death
HCM
Myocardial Fibrosis and risk of sudden death
•223 consecutive patients
•16 cardiac deaths at 3 years
Bruder, J Am Coll Cardiol 2010;56:875-887
HCM
Myocardial Fibrosis and risk of sudden death
•217 consecutive patients
•30 combined end-points
O’Hanlon, J Am Coll Cardiol 2010;56:867-74
HCM
Myocardial Fibrosis and risk of sudden death
Maron, J Cardiovasc Magnetic Res 2012, 14:13
Imaging in Hypertrophic
Cardiomyopathy
•Diagnosis
•Evaluation of Symptoms
•Screening
•Therapy Guidance
Risk of Sudden Cardiac Death
Relief of LVOT obstruction
HOCM
Myectomy
Intraoperative TEE in HCM