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ECHO 2013 / Systolic Heart Failure Review of Cardiomyopathy

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☆

Noncompaction of the LV

•Spongy cardiomyopathy, hypertrabeculation of the LV

–2:1 ratio noncompacted to compacted myocardium

•Fetal myocardial sinusoids fail to condense

•Isolated and nonisolated forms

•Progressive dilated cardiomyopathy

–VT (amiodarone/ICD)

–LV thrombi (anticoagulation therapy)

– End stage systolic function (transplantation)

Jenni et at, Heart 2001;86:666-671

Jenni et at, Heart 2001;86:666-671

Caution – as LV’s dilate normal trabeculations can look like noncompaction

Many roles of echocardiography in cardiomyopathy

•Diagnosis

•Prognosis

•Treatment – selection, guidance, response

–Response to medical therapy, revascularization

–Biventricular pacing, alcohol septal ablation

–Remodeling devices