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ECHO 2013 / Approach to Congenital Heart Disease The Unoperated Adult

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ECHOCARDIOGRAPHIC APPROACH TO CONGENITAL HEART DISEASE: THE UNOPERATED ADULT

Karen Stout, MD, FACC

Divisions of Cardiology

University of Washington Medical Center

Seattle Children’s Hospital

NO DISCLOSURES

CONGENITAL HEART DISEASE

DEFINITION

Heart disease present since birth

Atrial Septal Defect

Tetralogy of Fallot

Ventricular Septal Defect

Transposition of the great arteries

Atrioventricular Septal Defect

Truncus arteriosus

Congenital valvular stenosis

Valve atresia

Congenital valvular regurgitation

Single ventricle

Coarctation of the aorta

Anomalous pulmonary venous

Interrupted aortic arch

return

 

Etc.

INCIDENCE AND SURVIVAL OF CHD

0.8 % of live births

 

Before 1940

After 1940

 

 

 

 

 

90%

<10%

Inc/Yr

Less Severe Disease

Survival to 18

Severe Disease

Survival to 18

Total Adults/Yr

CONGENITAL HEART DISEASE

UNREPAIRED PALLIATED

ATRIAL SEPTAL DEFECT

VENTRICULAR SEPTAL DEFECT

PATENT DUCTUS ARTERIOSUS

ATRIOVENTRICULAR SEPTAL DEFECT

CONGENITALLY CORRECTED TRANSPOSITION OF THE GREAT VESSELS

TETRALOGY OF FALLOT

PULMONARY ATRESIA

SINGLE VENTRICLE

REPAIRED

ATRIAL SEPTAL DEFECT

VENTRICULAR SEPTAL DEFECT

PATENT DUCTUS ARTERIOSUS

ATRIOVENTRICULAR

SEPTAL DEFECT

TETRALOGY OF FALLOT

TRANSPOSITION OF THE

GREAT VESSELS SINGLE VENTRICLE

CONGENITAL HEART DISEASE

UNREPAIRED PALLIATED

ATRIAL SEPTAL DEFECT

VENTRICULAR SEPTAL DEFECT

PATENT DUCTUS ARTERIOSUS

ATRIOVENTRICULAR SEPTAL DEFECT

CONGENITALLY CORRECTED TRANSPOSITION OF THE GREAT VESSELS

TETRALOGY OF FALLOT

PULMONARY ATRESIA

SINGLE VENTRICLE

REPAIRED

ATRIAL SEPTAL DEFECT

VENTRICULAR SEPTAL DEFECT

PATENT DUCTUS ARTERIOSUS

ATRIOVENTRICULAR

SEPTAL DEFECT

TETRALOGY OF FALLOT

TRANSPOSITION OF THE

GREAT VESSELS SINGLE VENTRICLE

ROLE OF IMAGING

Evaluate anatomy

Chambers and valves

Extracardiac vasculature

Coronary anatomy

Evaluate ventricular function

Evaluate valvular function

Evaluate shunts

ESTABLISH

DIAGNOSIS

&

ESTABLISH IMPACT OF ABNORMALITY

ATRIAL SEPTAL DEFECT

ATRIAL SEPTAL DEFECT

anatomy

Secundum - 75%

Primum - 15-20%

Sinus venosus - 5-10%

Webb and Gatzoulis, Circulation 2006

ATRIAL SEPTAL DEFECT

anatomy

Secundum - 75%

Primum - 15-20%

Sinus venosus - 5-10%

Webb and Gatzoulis, Circulation 2006