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ECHO 2013 / Approach to Congenital Heart Disease The Postoperative Adult

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TETRALOGY OF FALLOT

ANATOMY

RIGHT VENTRICULAR OUTFLOW

TRACT OBSTRUCTION

VENTRICULAR SEPTAL DEFECT

OVERRIDING AORTA

RIGHT VENTRICULAR

HYPERTROPHY

TETRALOGY OF FALLOT

BLALOCK TAUSSIG THOMAS

SHUNT

“Make me a patent ductus arteriosus”

TETRALOGY OF FALLOT

BLALOCK TAUSSIG THOMAS

SHUNT

“Make me a patent ductus arteriosus”

Increases pulmonary blood flow → Decreases cyanosis

DEFINITIVE REPAIR – WALT LILLEHEI

TETRALOGY OF FALLOT

SURGICAL CORRECTION

Enlarge RVOT

Closure of VSD

Placement of

transannular patch

TETRALOGY OF FALLOT

SURGICAL CORRECTION

Not cyanotic

Normal pulmonary blood flow

Pulmonary insufficiency

Right ventricular enlargement

TRANSANNULAR

PATCH

TETRALOGY OF FALLOT

LONG TERM COMPLICATIONS

Pulmonary insufficiency and RV dysfunction

Transannular patch associated with significant PI

Arrhythmias

Supraventricular and ventricular

Sudden death Exercise intolerance

Decreased compared with age matched controls

TRANSTHORACIC ECHOCARDIOGRAM

Right heart size and function

Pulmonary regurgitation

Pulmonary stenosis

Left ventricular size and function

Aortic size and aortic valve function

ECHOCARDIOGRAM

PULMONARY STENOSIS AND REGURGITATION

ECHOCARDIOGRAM

RIGHT VENTRICULAR ENLARGEMENT