Ординатура / Офтальмология / Английские материалы / Strabismus A Decision Making Approach_Von Noorden, Helveston_1994
.pdf(3)Measurements of the deviation in the diagnostic positions of gaze establish which of the vertical rectus or oblique muscles are overacting or underacting and establish whether the strabismus is incomitant (see
2.14, 2.15, and 2.21).
(4)The forced duction test determines whe ther the strabismus is caused by innervational factors (paralysis or paresis) or restrictive factors (see 1.30).
(5)In muscle paralysis of recent onset the forced duction test result is negative.
(6)Dissociated vertical deviations (DVD) differ in several aspects from true hyperdeviations (see 2.16) and may coexist with hypertropia and A or V patterns.
(7)Comitant hyperdeviations are rare. It is unusual to find a patient with a significant hyperdeviation of the same magnitude in all gaze positions. In many instances such patients may have at one time had a paretic cyclovertical deviation that became comitant over time. In others, the hypertropia may have been caused by inadvertent raising or lowering of the muscle insertions during a previous operation for horizontal strabismus.
(8)Paralytic strabismus, although incomitant in its initial stage, may become increasingly comitant with the passage of time.
(9)(See 2.30). An acquired comitant vertical deviation is called skew deviation. It usually occurs in an older individual and is caused by a brainstem microvascular insult. The condition may be self-limiting. If not, it may be treated at least temporarily with vertical prism. The deviation is usually of small amplitude, being less than 10 prism diopters. Persistent skew deviation may be treated with recession of one or more vertical rectus muscles.24, p.520
Section 1: Preliminaries - 1.25 Anomalous Head Posture
An anomalous head posture becomes readily apparent during the initial part of the e xamination. In children it is best observed under casual conditions (e.g., while directing attention to the parents while the history is obtained). The parents or the patient may be unaware of an anomalous head posture. In most instances of incomitant strabismus, the head is rotated to avoid diplopia. For this reason, an anomalous position is often referred to as a "compensatory" head posture. Less frequently and when fusion becomes impossible or is difficult to maintain, the head is rotated such that the separation between the double images is maximized (paradoxic head posture).71 An ocular head tilt or head turn unrelated to incomitant strabismus occurs with nystagmus and a null point in certain gaze positions. Another ocular cause, unrelated to an ocular motility problem, is an uncorrected refractive error. When obtaining the history it is important to ascertain whether the anomalous posture is constant, if its direction is always the same, and whether it occurs at all or only at certain fixation distances. An anomalous head posture should always raise concern because it may cause neck strain; if left untreated, secondary scoliosis, contracture of the neck muscles, 58, p.317 and facial asymmetry75 may occur.
(1)See 1.26.
(2)See 1.27.
(3)See 1.28 and 1.29.
(4)See 1.26, 1.27, 1.28 and 1.29.
Section 1: Preliminaries - 1.26 Head Turn
A patient turns his or her head (face) to one side and looks to the opposite side for two reasons: (1) He or she is unable to look to one side and therefore looks to the other side, or (2) he or she chooses to look to one side because it is more comfortable, improves visual acuity, or avoids diplopia. While most head turns are caused by strabismus or nystagmus, an uncorrected refractive error or a unilateral hearing defect may also have to be considered as causes.
(1)The patient turns his or her face to use an eye position in which the nystagmus is least pronounced (null point, neutral zone). In that position visual acuity is optimal but decreases when the head is passively straightened. In casual seeing the eyes (head) may be straight, but when looking at smaller objects or during visual attention (e.g., during visual acuity testing or while watching TV), the face turn is accentuated. Periodic alternating nystagmus causes an alternating face turn (see 2.33 and 2.34). 24, p. 542
(2)Patients with essential infantile esotropia and manifest latent nystagmus frequently prefer to hold their dominant eye in a position of extreme adduction. The reason for this is that the nystagmus is generally
dampened in this gaze position. A head turn in the direction of the fixating eye consequently develops.24,
p.421; 70
(3)Dissociated vertical or horizontal deviations may be associated with a head turn (see 2.16).
(4)In other cases the nose may be used to "occlude" the adducted eye to avoid double vision. The head is turned toward the side of the adducted eye.
(5)When an eye cannot adduct or abduct, the patient usually fixates in a gaze position opposite to that of the restricted duction. This allows the eye with restricted abduction or adduction some horizontal range of movement. For instance, when abduction is limited the preferred gaze position is one of adduction. The head turn is usually used to avoid diplopia.
(6)In some cases of unilateral third nerve palsy, the patient fixates with the paralyzed eye and the fello w eye may be amblyopic. In such cases, the head is turned toward the nonparalyzed side (see 2.36).
(7)In cases of Duane syndrome type II with exotropia, the face is turned away from the involved eye, a response opposite to the more common Duane syndrome type I with esotropia and a head turn toward the side of the involved eye (see 2.50, 2.51, and 2.52). A head turn may be seen in any of the classes of Duane syndrome.
Section 1: Preliminaries - 1.27 Head Tilt to Either Shoulder
(1)A patch is placed over the right and then the left eye while the patient is observed for changes in the head posture. Patients with nonocular head tilt do not respond to the patch test. The patient is encouraged to sit up straight during this observation. The patient's attention is directed toward a distant fixation target. It is important that he or she be unaware of the purpose of the te st and remain relaxed during observation. In children it is advisable to ask the child to walk to the end of the room and back.
(2)The head tilt compensates for the tilt of the visual environment. It disappears on patching of the eye with cyclotropia.
(3)A compensatory head posture with the chin elevated and pointing toward the opposite shoulder permits fusion in Brown syndrome.24, p.408; 58, p.404
(4)The head tilt, often in combination with a face turn, avoids diplopia in cyclovertical strabismus. Infrequently, the head is tilted to cause maximal separation of the double images when fusion cannot be maintained.71 The direction of the head tilt is of no diagnostic significance. Patching one eye eliminates diplopia and the head straightens.
(5)Congenital nystagmus with null point in tertiary gaze may cause a head tilt to either shoulder. The patient has optimal visual acuity with the head tilted. The nystagmus may be of minimal amplitude and escape detection.68
(6)A long-standing ocular head tilt may cause tightness of the neck muscles, deformities of the cervical spine,58, p. 371 and facial asymmetry.75 These sequelae of ocular head tilt may maintain an abnormal head posture even after the ocular cause has been removed.
(7)Fibrosis of the sternocleidomastoid muscle may be caused by intramuscular hemorrhage during birth. Unlike ocular head tilt, the congenital torticollis may be present as early as 6 months after birth. The tightness of the muscle is palpable and prevents passive tilting of the head toward the noninvolved side.
(8)This unusual cause of a severe head tilt56 should be considered the differential diagnosis.
Section 1: Preliminaries - 1.28 Chin Elevation
(1) A patient may assume a chin-up anomalous head posture because comfortable binocular vision or improved visual acuity can be obtained when both eyes are in a position of depression. The primary position of the eyes is avoided because double vision or decreased visual acuity may be present in that position.
(2) The first diagnostic step should determine whether both eyes elevate normally. If they do, vertical strabismus from innervational or mechanical restrictive causes can be excluded.
(3)When the cover test (see 1.16) shows a heterotropia in upward gaze and no shift on covering either eye in downward gaze, horizontal strabismus with incomitance in vertical gaze (A or V pattern) is present. Some patients may note double vision when the head is passively straightened but not when the chin is elevated.
(4)The prism cover test is performed with the fixation target in 30 degree elevation and depression to diagnose an A or V pattern strabismus24, p.535; 58, p.358 (see 2.22 and 2.23).
(5)Manifest nystagmus is usually diagnosed by direct observation. Occasionally, the nystagmus amplitude may be so small that it escapes casual clinical examination and can only be diagnosed with magnifi cation by ophthalmoscopy or biomicroscopy (micronystagmus) (see 2.33).
(6)Congenital or acquired nystagmus may have a null point with the eyes in depression. In that case, the patient elevates the chin to gain be tter vision. This improvement may be too subtle to measure on the
acuity chart but sufficiently important for the patient to maintain an uncomfortable head posture. 24, p. 541
(7)See 2.33.
(8)Forced ductions must be performed when examination of ductions and versions shows limitation of elevation of the eye(s). In most instances such limitations indicate mechanical restriction of elevation from a number of causes listed below. In cooperative subjects the test is performed in the office after local anesthesia is obtained with topical 4% lidocaine hydrochloride. It is important to instruct the patient to look up while determining whether there is a restriction to elevation.
(9)Restriction of elevation from endocrine myopathy of the inferior rectus muscle is usually asymmetric.
However, in most instances both eyes are involved and surgery on both eyes may be required (see
2.55).24, p.489; 58, p. 410
(10)See 2.54.
(11)See 2.29.
(12)See 2.53.
(13)See 2.37 and 2.40.
Section 1: Preliminaries - 1.29 Chin Depression